Alveolus protein deposits _'s general knowledge of disease

Alveolus protein deposits _'s general knowledge of disease
Summary
Alveolus protein deposit disease ' Abbreviated as PAP) ,Also called Rosen-Castle-man-Liebow syndrome. Full of PAS and dye the masculine gender in alveolus and thin bronchus, rich phosphatide protein material from lung is its characteristic. Good hair, on blue and green middle age, man have illness coming on about 3 times as much as that of woman
Cause of disease
Bright, may with the intersection of immunological function and obstacle (until thymus wither and immune defect, lymphocyte reduce etc.) Have something to do. The dust can cause PAP in order to contact the animal of the silicious dust particularly, so think it may be to some non- peculiar responses of stimulating the thing, cause alveolus macrophages to decompose, produce PAS positive protein.
Symptom
Onset much latent to attack, typical symptom for out of breath behind the activity, develop to feel out of breath also have a rest, later, cough white or yellow phlegm, weak and becoming thin. Continue and take place it while infecting, there is generating heat, suppuration phlegm.
Check
There can not be symptom in a few cases, only the X-ray unusually behaves. The breathing function obstacle is aggravated as the condition is developed, dyspneal companion's cyanosis also becomes serious.
Treat
How directed primarily to to remove the calm albumen - like material in the alveolus. Use one pair of tracheas conduit (Carlen conduit) in recent years Or fine to prop up mirror, make one side lung or physiological saline of lobe of the lung, irritate and wash, hocket regularly. Recent curative effect reveals patient's dyspnea and lung function improve, half the number patient X-ray chest slice is variable and clear. The long-term result majority keeps relieving the state, a few patients recur, often within 6- 24 months, can make the lung to irritate and wash again.
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